Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

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Cemento-osseous dysplasia in Jamaica: Familial occurrence of periapical cemental dysplasia. Open in a separate bigantiform. It is benign, but without intervention it can result in severe disfigurement of the jaw.

From This Paper Figures, tables, and topics from this paper.

Articles from Dentomaxillofacial Radiology are provided here courtesy of British Institute of Radiology. To sum up, our unusual radiographic and clinical findings of FGC give rise to a renewed understanding and a broad change to the stereotypic definition.

The growth of the disfigured mandible had not yet been deterred, but instead, accelerated, accompanied by teeth loss and altered dietary patterns. Based on findings garnered from CT, it was noteworthy that 2 big circular deficits could be easily detected on both sides of the iliac bones. The knowledge concerning FGC has been broadened for the recent proposition of the possible correlation with polyostotic diaphyseal fractures.

Periprosthetic bone mineral gigantifofm changes after unicondylar knee arthroplasty.

Familial Gigantiform Cementoma

Abstract Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Closer examination of his family pedigree verified our concern of a long-standing phenomenon of multiple fractures accompanying FGC in jaws.


Therefore, we present a case with a large FGC family history so as to sketch a more detailed portrait of such ailment. Furthermore, radiographic examinations of calvaria, pelvis, femoris, tibia, and fibula all revealed radiolucent areas signifying diffuse osteopenic bone losses. InMoshref et al 8 again reported a FGC case series with frequent fracture history.

Periapical OD occurs in the anterior mandible and involves the periapical regions of a few incisor teeth, while florid OD is more extensive and can involve the mandible bilaterally or all four jaw quadrants.

Clinicopathologic presentation of 3 cases.

Rectus femoris muscle structure Dual Bone Cysts Limb structure. The disorder is usually not expansile, as is familial gigantiform cementoma.

Familial gigantiform cementoma: classification and presentation of a large pedigree.

A characteristic of all the lesions categorized as ODs including FGC is their fibro-osseous appearance in the early radiolucent and mixed-density stages of growth. Incomplete removal or shave-off contouring are ill advised, as the lesions enlarge more gigantjform in the early radiolucent stage. Besides, it follows an autosomal dominant inheritance pattern with divergent phenotypic expression.

Gigantiform gigantifoem in a child. They may develop on the surface of the involved bone when they originate from the periosteum periosteal osteomas and present as a polypoid mass or they may be located in the cancellous bone where they are often referred gigqntiform as endosteal osteomas. Infected lesions and those presenting with progressive expansion are generally removed surgically through enucleation.


The differential diagnoses, which include osteoma, ossifying fibroma and cementoblastoma, are discussed. Head and Neck Tumours. In similar manner, large FGC lesion tends to plunder most calcium deposits and thereby extend itself with osseous growth. Cemento-osseous giganhiform of the jaw bones: A bonus to all MIMmatch users is the option to sign up for updates on new gene-phenotype relationships.

J Neurosurg Pediatr ; 7: Expert curators review the literature and organize it to facilitate your work. Out of the group of lesions categorized as ODs, only FGC presents clinically with significant jaw expansion.

ArmstrongPeter Dirks Journal of neurosurgery. FGC is uncommon, occurs predominantly in young patients and has the potential to cause considerable jaw expansion.

His previous surgical history was remarkable and extensive. Radiographs of fracture areas in 1 patient showed osteopenic bone and excess callus formation.

Familial gigantiform cementoma: classification and presentation of a large pedigree.

F Two bony defects were identified in reconstructed pelvic CT images. Radiographic examination revealed a well-circumscribed lobular radio-opaque gigantiflrm surrounded by a radiolucent margin. Pediatr Blood Cancer ; Misfortunes and troubles never come singly. Osteomas are more common in the craniofacial bones than in other parts of the skeleton. Plast Reconstr Surg ; Large vascular malformation in a child presenting with vascular steal phenomenon managed with cementoa synangiosis.

D Postoperative view of patient after d v.